| 1 |
Primary Arterial Hypertension |
| |
1.1 |
Primary Pulmonary Hypertension
[02/16/2006 Editor's note: This is an older classification and is no longer used to identify people with no known cause for the PAH] |
| |
|
(a) |
Sporadic |
| |
|
(b) |
Familial |
| |
1.2 |
Related to: |
| |
|
(a) |
Collagen Vascular Disease |
| |
|
(b) |
Congenital Systemic to Pulmonary Shunts |
| |
|
(c) |
Portal Hypertension |
| |
|
(d) |
HIV Infection |
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|
(e) |
Drugs/Toxins |
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|
|
(1) |
Anorexigens |
| |
|
|
(2) |
Other |
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|
(f) |
Persistent Pulmonary Arterial Hypertension of the Newborn |
| |
|
(g) |
Other |
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|
|
|
|
|
|
|
| 2 |
Pulmonary Venous Hypertension |
| |
2.1 |
Left-Sided Atrial or Ventricular Heart Disease |
| |
2.2 |
Left-Sided Valvular Heart Disease |
| |
2.3 |
Extrinsic Compression of Central Pulmonary Veins |
| |
|
(a) |
Fibrosing Mediastinitis |
| |
|
(b) |
Adenopathy/Tumors |
| |
2.4 |
Pulmonary Veno-Occlusive Disease |
| |
2.5 |
Other |
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|
|
|
| 3 |
Pulmonary Arterial Hypertension Associated with Disorders of the Respiratory System and/or Hypoxemia |
| |
3.1 |
Chronic Obstructive Pulmonary Disease |
| |
3.2 |
Interstitial Lung Disease |
| |
3.3 |
Sleep Disordered Breathing |
| |
3.4 |
Alveolar Hypoventilation Disorders |
| |
3.5 |
Chronic Exposure to High Altitude |
| |
3.6 |
Neonatal Lung Disease |
| |
3.7 |
Alveolar-Capillary Dysplasia |
| |
3.8 |
Other |
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|
|
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| 4 |
Pulmonary Arterial Hypertension due to Chronic Thrombotic and/or Embolic Disease |
| |
4.1 |
Thromboembolic Obstruction of Proximal Pulmonary Arteries |
| |
4.2 |
Obstruction of Distal Pulmonary Arteries |
| |
|
(a) |
Pulmonary embolism (Thrombus, Tumor, OVA and/or parasites, Foreign Material) |
| |
|
(b) |
In-situ Thrombosis |
| |
|
(c) |
Sickle Cell Disease |
| |
|
|
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| 5 |
Pulmonary Arterial Hypertension due to Disorders Directly Affecting the Pulmonary Vasculature |
| |
5.1 |
Inflammatory |
| |
|
(a) |
Schistosomiasis |
| |
|
(b) |
Sarcoidosis |
| |
|
(c) |
Other |
| |
5.2 |
Pulmonary Capillary Hemangiomatosis |
